Overview of Rare Bleeding Disorders

An Overview of Rare Bleeding Disorders: Factors VII and Factors XIII Deficiencies

ISTH 2015 (Toronto, June 20-25) A discussion session on rare bleeding disorders was conducted at the International Society on Thrombosis and Hemostasis (ISTH) 2015 Meeting. During the discussion on FXIII deficiency, it was stressed that all children should be on prophylaxis because of the risk of life-threatening bleeding, and the goal is to keep the patient’s FXIII level at 30%. During the FVII deficiency part of the discussion, it was mentioned that there are two types of bleeders: the “platelet type” which tend to bleed in the mucosal and skin area and the “hemophilia type” who tend to experience joint bleeding and hematomas, a localized collection of blood. It was suggested that the “hemophilia type” should be on treatment.